鞍山地区2013年1月～2018年1月血友病诊疗的临床回顾分析

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Abstract Objective To analyze the clinical features,diagnostic age and replacement therapy pattern of patients with hemophiliain in Anshan.Methods The clinical data of 64 patients with hemophilia treated in Anshan Hospital,the First Affiliated Hospital of China Medical University from January 2013 to January 2018 were retrospective analyzed.Results All patients were male,47 patients had been treated in hospital,43 cases had hemophilia A and 4 cases had hemophilia B.27 patients(57.45%)had family history of hemophilia.The median age of the first diagnosed was 5 years old.The diagnostic timing was related to the severity of the first hemorrhage(P＝0.0033).18 cases(38.30%)of the hospitalized patients had different degree of joint deformity.Most of the registered patients were treated on demand.There was no strict preventive treatment.Conclusion There are 64 cases of hemophilia in Anshan.The diagnosis age is delayed and the replacement therapy is not enough.The timing of diagnosis is related to the degree of first bleeding,and the incidence of joint deformity is high.

Key words： Hemophilia Joint damage Replacement therapy

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	Articles by authors
	YAN Chao-qi
	LENG Qing
	YOU Guo-ping
	ZHANG Li-jun

Cite this article:

YAN Chao-qi,LENG Qing,YOU Guo-ping, et al. Clinical retrospective analysis of 64 patients with hemophilia in 5 recent years in Anshan[J]. 中国当代医药, 2018, 25(21): 158-160.

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http://dangdaiyiyao.com/EN/ OR http://dangdaiyiyao.com/EN/Y2018/V25/I21/158

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